Spongiform encephalopathy
Common Name(s)
Spongiform encephalopathy, Gerstmann Straussler Scheinker syndrome, Gerstmann-Straussler-Scheinker disease, Amyloidosis cerebral with spongiform encephalopathy
Advocacy and Support Organizations
Condition Specific Organizations
Following organizations serve the condition "Spongiform encephalopathy" for support, advocacy or research.
How do you compare to others with this condition?
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Advocacy and Support Organizations
Condition Specific Organizations
Following organizations serve the condition "Spongiform encephalopathy" for support, advocacy or research.
Recommended Apps
Anonymously share and see how your answers compare with others with this condition while privately providing key pieces of information to medical researchers, disease advocacy groups, and others ONLY YOU select to help speed up cures and better alternatives.
Finding the right clinical trial for Spongiform encephalopathy can be challenging. However, with TrialsFinder (which uses the Reg4ALL database and privacy controls by Private Access), you can permit researchers to let you know opportunities to consider - all without revealing your identity.
Scientific Literature
Articles from the PubMed Database
Research articles describe the outcome of a single study. They are the published results of original research.
The terms "Spongiform encephalopathy" returned 89 free, full-text research articles on human participants.
First 3 results:
Journal:
Conformational conversion of the cellular isoform of prion protein, PrP, into the abnormally folded, amyloidogenic isoform, PrP, is a key pathogenic event in prion diseases, including Creutzfeldt-Jakob disease in humans and scrapie and bovine spongiform encephalopathy (BSE) in animals. ...
Journal: Emerging Infect. Dis.. 2017 09;23(9):1522-1530.
Bovine spongiform encephalopathy (BSE) is the only known zoonotic prion that causes variant Creutzfeldt-Jakob disease (vCJD) in humans. The major risk determinant for this disease is the polymorphic codon 129 of the human prion protein (Hu-PrP), where either methionine (Met) or valine ...
Journal:
Aggregation of misfolded proteins or peptides is a common feature of neurodegenerative diseases including Alzheimer's, Parkinson's, Huntington's, prion and other diseases. Recent years have witnessed a growing number of reports of overlap in neuropathological features that were once ...
To view other free, full-text articles on human participants, please click on the link below.
Reviews from the PubMed Database
Review articles summarize what is currently known about a disease. They discuss research previously published by others.
The terms "Spongiform encephalopathy" returned 21 free, full-text review articles on human participants.
First 3 results:
Journal: Prion. ;7(5):420-33.
Since the appearance in 1986 of epidemic of bovine spongiform encephalopathy (BSE), a new form of neurological disease in cattle which also affected human beings, many diagnostic and research activities have been performed to develop detection and therapeutic tools. A lot of progress ...
Journal: Folia Neuropathol. 2009 ;47(2):95-103.
The subject of transmissible spongiform encephalopathy may properly be said to have begun with the experimental transmission of scrapie by Cuillé and Chelle in 1936, although Creutzfeldt and Jakob had described the disease that bears their names in 1920-21. Thirty more years passed ...
Journal: Med Sci (Paris). 2007 Dec;23(12):1148-57.
Bovine spongiform encephalopathy (BSE) is a transmissible spongiform encephalopathy (TSE) identified twenty years ago in the British cattle herds. Creutzfeldt-Jakob disease (CJD) is a TSE that occurs in humans. In 1996, scientists found a possible link between BSE and a new variant ...
To view other free, full-text review articles on human participants, please click on the link below.
Symptoms, Diagnosis, and Treatment
https://ghr.nlm.nih.gov/condition/glycine-encephalopathy
https://ghr.nlm.nih.gov/condition/ethylmalonic-encephalopathy
https://ghr.nlm.nih.gov/condition/chd2-myoclonic-encephalopathy
https://ghr.nlm.nih.gov/condition/mitochondrial-neurogastrointestinal-encephalopathy-disease
https://ghr.nlm.nih.gov/condition/stxbp1-encephalopathy-with-epilepsy
https://ghr.nlm.nih.gov/condition/biotin-thiamine-responsive-basal-ganglia-disease
https://ghr.nlm.nih.gov/condition/mecp2-related-severe-neonatal-encephalopathy
https://ghr.nlm.nih.gov/condition/acute-necrotizing-encephalopathy-type-1
https://ghr.nlm.nih.gov/condition/scn8a-related-epilepsy-with-encephalopathy
https://ghr.nlm.nih.gov/condition/early-infantile-epileptic-encephalopathy-1
https://ghr.nlm.nih.gov/gene/STXBP1
https://ghr.nlm.nih.gov/condition/cdkl5-deficiency-disorder
https://ghr.nlm.nih.gov/condition/genetic-epilepsy-with-febrile-seizures-plus
https://ghr.nlm.nih.gov/gene/RANBP2
https://ghr.nlm.nih.gov/gene/SCN8A
https://ghr.nlm.nih.gov/condition/leigh-syndrome
https://ghr.nlm.nih.gov/condition/grin2b-related-neurodevelopmental-disorder
https://ghr.nlm.nih.gov/gene/ETHE1
https://ghr.nlm.nih.gov/gene/SLC25A22
Clinical Trial Information This information is provided by ClinicalTrials.gov
Condition Summary: Prion Diseases
Condition Summary: Creutzfeldt-Jakob Syndrome
Finding the right clinical trial for Spongiform encephalopathy can be challenging. However, with TrialsFinder (which uses the Reg4ALL database and privacy controls by Private Access), you can permit researchers to let you know opportunities to consider - all without revealing your identity.