Stargardt disease 1 is a condition that causes progressive vision loss. It affects a small part of the eye called the macula, which is located in the retina. The macula is responsible for sharp central vision, which means it is important for reading, driving, and recognizing faces. With stargardt disease 1, a fatty yellow substance builds up in the cells in the macula, which eventually damages the cells. The disease becomes worse over time, and eventually leads to difficulty seeing at night or in low light situations. Problems with color vision are also known to be a symptom of stargardt 1.
The symptoms usually occur in late childhood to early adulthood, and the progression of the disease varies widely among individuals with stargardt 1. It is a genetic disease that is passed from a parent to their child. It is diagnosed with multiple eye exams, and can be confirmed with genetic testing.
There is currently no treatment for this disease, but precautions to slow the advancement of the disease include avoiding overexposure to light (such as wearing sunglasses when possible), and avoiding the consumption of vitamin A supplements. People with this disease cannot break down vitamin A in the retina causing a build up of vitamin A, which is toxic to the eyes. Regular visits to eye doctors are recommended in order to monitor the progress of the disease. If you have been diagnosed with this condition, talk to your doctor about the the best options for you.
Description Last Updated: Jan 15, 2018